Consultez les derniers articles autour de la maladie de Willebrand
Dernière mise à jour : Vendredi 06 juin 2025Haemorrhagic episodes may have physical or psychological effects on children with von Willebrand disease (VWD) and their families. These effects can be measured by health-related quality of life (HRQoL)....
Lire la suite
Von Willebrand disease (VWD) type 2 arises from variants in von Willebrand factor (VWF) that disrupt its essential hemostatic functions. Per ISTH guidelines, it is classified as type 2A, 2B, 2M, and 2N...
Lire la suite
Congenital von Willebrand disease can be autosomal recessive or dominant and is classified into types 1, 2, and 3, based on laboratory findings. Severe von Willebrand factor deficiency (type 3 von Willebrand...
Lire la suite
This report describes a 55-year-old man with hypertension, hypercholesterolemia, type 2B von Willebrand disease (VWD2B), and thrombocytopenia requiring 2 surgical total hip replacements managed with pure von Willebrand factor (VWF) concentrate (Wilfactin®) and VWF/Factor VIII (FVIII) complex concentrate (Voncento®). VWD2B is a rare, autosomal-dominant, inherited disorder of primary hemostasis caused by VWF alterations that increase its affinity...
Lire la suite
3 DDAVP response and its determinants in bleeding disorders: a systematic review and meta-analysis
Blood 2025; 145(16): 1814-25