Consultez les derniers articles autour de la maladie de Willebrand
Dernière mise à jour : Jeudi 23 mai 2024Von Willebrand disease (VWD) is the most common inherited bleeding disorder, characterized by either partial or complete von Willebrand factor (VWF) deficiency or by the occurrence of VWF proteoforms of...
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Four variants have been continuously subjected to debate and received different von Willebrand disease (VWD) classifications: p.R1315L, p.R1315C, p.R1374H, and p.R1374C. We chose to comprehensively investigate...
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Von Willebrand disease (VWD) is the most prevalent inherited bleeding disorder (BD), affecting up to 1% of the general population. Over 75% of women with VWD experience heavy menstrual bleeding (HMB),...
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There is significant ongoing debate regarding type 1 von Willebrand disease (VWD) defintion. Previous guidelines recommended patients with von Willebrand factor (VWF) levels <30 IU/dL be diagnosed type 1 VWD, whereas patients with significant bleeding and VWF levels from 30 to 50 IU/dL be diagnosed with low VWF. To elucidate the relationship between type 1 VWD and low VWF in the context of age-induced increases in VWF levels, we combined data sets...
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3 Diagnosis and treatment of von Willebrand disease in 2024 and beyond
Haemophilia 2024; 30(S3): 103-11